A Sporadic Association Of Naevus Spilus And Neurofibromatosis (Type 5) - A Case Report

Abstract

Nevus spilus, also known as speckled lentiginous nevus or nevus on nevus, are congenital nevus with uniformly coloured hyper-pigmented patchy background, superimposed with multiple dark pigmented spots. Two different types of nevus spilus have been reported in the literature, namely nevus spilus maculosa and nevus spilus papulosa.  Our patient along with naevus spilus had segmental café-au-lait macules and neurofibroma affecting more than one dermatome which according to Riccardi’s classification, comes under NF-type5. There are reports of the association of nevus spilus with neurofibromatosis 1 in literature . But there are no reports of association of nevus spilus and segmental NF in the same patient.